Panniculitis in Anti-MDA-5 Positive Juvenile Dermatomyositis: A Case Report
Journal of the Nepal Medical Association, cilt.63, sa.281, ss.61-64, 2025 (SCI-Expanded)
- Yayın Türü: Makale / Tam Makale
- Cilt numarası: 63 Sayı: 281
- Basım Tarihi: 2025
- Doi Numarası: 10.31729/jnma.8874
- Dergi Adı: Journal of the Nepal Medical Association
- Derginin Tarandığı İndeksler: Science Citation Index Expanded (SCI-EXPANDED), Scopus, IBZ Online, CAB Abstracts, Directory of Open Access Journals
- Sayfa Sayıları: ss.61-64
- Anahtar Kelimeler: anti MDA-5, dermatomyositis, panniculitis
- Çanakkale Onsekiz Mart Üniversitesi Adresli: Evet
Özet
Panniculitis is a rare clinical finding in dermatomyositis. There are few reported cases in the medical literature. In this report, we describe a 17-year-old male patient with anti-MDA5 positive hypomyopathic dermatomyositis who, eight months after diagnosis, presented with indurated nodules on the right forearm and right thigh despite methotrexate and monthly intravenous immunoglobulin treatment. A skin biopsy revealed lobular panniculitis with lymphocytic infiltrate. His lesions were successfully controlled with hydroxychloroquine and azathioprine. This article presents a case regarding the rarity of panniculitis in juvenile dermatomyositis and its treatment strategy.