Pulmonary lymphangitic sarcomatosis and a review of the literature

Gönlügür T., Güneç Sapmaz F., Katrancıoğlu Ö., Gönlügür U., Elagöz Ş.

CLINICAL AND EXPERIMENTAL METASTASIS, cilt.26, sa.5, ss.399-402, 2009 (SCI-Expanded)

  • Yayın Türü: Makale / Vaka Takdimi
  • Cilt numarası: 26 Sayı: 5
  • Basım Tarihi: 2009
  • Dergi Adı: CLINICAL AND EXPERIMENTAL METASTASIS
  • Derginin Tarandığı İndeksler: Science Citation Index Expanded (SCI-EXPANDED), Scopus
  • Sayfa Sayıları: ss.399-402
  • Çanakkale Onsekiz Mart Üniversitesi Adresli: Evet

Özet

Intrapulmonary spread of a sarcoma via lymphatics is a rare cause of death in a young adult. A 31-year old man was admitted to our hospital complaining of dyspnea and malaise of 2 months' duration. A chest radiography revealed bilateral hilar enlargement, and reticulonodular infiltrations. Thoracic CT-scans demonstrated mediastinal lymphadenopathy, thickening of interlobular septa, polygonal lines, and thickening of bronchovascular bundles. The diagnosis was made by open-lung biopsy. The patient died within 3 months after diagnosis. Pulmonary lymphangitic sarcomatosis is a rare but important manifestation of an angiosarcoma. Optimal treatment of these patients is not well defined, but a trial of chemotherapy may be warranted.